Copyright © 1987 by the European Society of Cardiology.
© 1987 The European Society of Cardiology
An infant with the scimitar syndrome and pulmonary hypertension; successful surgical intervention


*Section of Paediatric Cardiology, Department of Paediatrics, Academisch Medisch Centrum Amsterdam, The Netherlands
Section of Paediatric Cardiosurgery, Department of Surgery, Academisch Medisch Centrum Amsterdam, The Netherlands
Ospedale Pediatrico Bambino Gesu Roma.
Received 28 April 1986; revised 21 July 1986; .
Address for correspondence: R. F. H. M. Tummers, Pediatrician, Ziekenhuis Ziekenzorg, Haaksbergerstraat 55, NL-7513 ER Enschede, The Netherlands.
Abstract
The case of an infant with the scimitar syndrome and pulmonary hypertension is presented. After surgical intervention with ligation of the abnormal arterial supply to the hypoplastic lung, the pulmonary hypertension disappeared. This was proven by cardiac catheterization after the operation. The abnormal drainage from the right lung into the inferior vena cava was not corrected. The child has had no complaints since except for recurrent pulmonary infections.
Key Words: Scimitar syndrome pulmonary hypertension.