American College of Cardiology/European Society of Cardiology Clinical Expert Consensus Document on Hypertrophic Cardiomyopathy: A report of the American College of Cardiology Foundation Task Force on Clinical Expert Consensus Documents and the European Society of Cardiology Committee for Practice Guidelines

doi:10.1016/S0195-668X(03)00479-2

European Heart Journal 2003 24(21):1965-1991; doi:10.1016/S0195-668X(03)00479-2
Copyright © 2003 by the European Society of Cardiology.

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ACC/ESC Expert consensus document

American College of Cardiology/European Society of Cardiology Clinical Expert Consensus Document on Hypertrophic Cardiomyopathy

A report of the American College of Cardiology Foundation Task Force on Clinical Expert Consensus Documents and the European Society of Cardiology Committee for Practice Guidelines

Writing Committee Members, Barry J. Maron, (Co-Chair)^a,b, William J. McKenna, (Co-Chair)^a,b^,*, Gordon K. Danielson^a, Lukas J. Kappenberger^a,b^,*, Horst J. Kuhn^b^,*, Christine E. Seidman, Pravin M. Shah^a, William H. Spencer, III^a, Paolo Spirito^a,b^,*, Folkert J. Ten Cate^a,b^,* and E. Douglas Wigle^a

ACCF Task Force on Clinical Expert Consensus Documents Members, Robert A. Vogel, (Chair), Jonathan Abrams, Eric R. Bates, Bruce R. Brodie, Peter G. Danias, Gabriel Gregoratos, Mark A. Hlatky, Judith S. Hochman, Sanjiv Kaul, Robert C. Lichtenberg, Jonathan R. Lindner, Robert A. O’Rourke, Gerald M. Pohost, Richard S. Schofield, Cynthia M. Tracy and William L. Winters, Jr

ESC Committee for Practice Guidelines Members^*, Werner W. Klein, (Chair), Silvia G. Priori, (Co-Chair), Angeles Alonso-Garcia, Carina Blomström-Lundqvist, Guy De Backer, Jaap Deckers, Markus Flather, Jaromir Hradec, Ali Oto, Alexander Parkhomenko, Sigmund Silber and Adam Torbicki

The first 150 words of the full text of this article appear below.

Table of contents

Preamble

Introduction

Organizationof committee and evidencereview

Purposeof this Expert Consensus Document

General considerations andperspectives

Nomenclature, definitions, and clinical diagnosis

Obstruction to LV Outflow

Genetics and molecular diagnosis

General considerations for natural history, and clinical course

Symptoms and pharmacological managementstrategies

Beta-adrenergicblocking agents

Verapamil

Disopyramide

Drugs in end-stage phase

Asymptomaticpatients

Infective endocarditis prophylaxis

Pregnancy

Treatment options fordrug-refractory patients

Additional approaches to relieveoutflowobstruction and symptoms

Dual-chamberpacing

Percutaneous alcohol septalablation

Sudden Cardiac Death

Riskstratification

Prevention

Athleterecommendations

Atrial Fibrillation

References

Preamble

This document has been developed as a Clinical Expert ConsensusDocument (CECD), combining the resources of the American Collegeof Cardiology Foundation (ACCF) and the European Society ofCardiology (ESC). It is intended to provide a perspective onthe current state of management of patients with hypertrophiccardiomyopathy. Clinical Expert Consensus Documents are intendedto inform practitioners, payers, and other interested partiesof . . . [Full Text of this Article]

Introduction

Organization of committee and evidence review
Purpose of this Expert Consensus Document
General considerations and perspectives

Nomenclature, definitions, and clinical diagnosis

Obstruction to LV Outflow

Genetics and molecular diagnosis

General considerations for natural history, and clinical course

Symptoms and pharmacological management strategies

Beta-adrenergic blocking agents
Verapamil
Disopyramide
Drugs in end-stage phase
Asymptomatic patients
Infective endocarditis prophylaxis
Pregnancy
Treatment options for drug-refractory patients

Additional approaches to relieve outflow obstruction and symptoms

Dual-chamber pacing
Percutaneous alcohol septal ablation
Sudden Cardiac Death

Risk stratification
Prevention
Athlete recommendations
Atrial Fibrillation

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