Copyright © 1995 by the European Society of Cardiology.
© 1995 The European Society of Cardiology
Isolated pulmonary vein stenosis in complex congenital heart disease, simulating cor triatriatum by cardiac catheterization and transoesophageal echocardiography

*Department of Pediatrics, Division of Pediatric Cardiology Rotterdam, The Netherlands
Department of Cardio-Thoracic Surgery, Sophia Children's Hospital, University Hospital Rotterdam, The Netherlands
Received 22 February 1994; revised 8 August 1994; accepted 10 August 1994.
Correspondence: A. H Cromme-Dijkhuis, MD, Department of Pediatrics, Division of Pediatric Cardiology, Sophia Children's Hospital, dr. Molenwaterplein 60, 3015 GJ, Rotterdam, The Netherlands.
Abstract
A case of localized stenosis of the lower left pulmonary vein, associated with perimembranous ventricular septal defect (VSD) and secundum atrial defect (ASD), a borderline sized mitral valve apparatus and left ventricle, is described This final diagnosis was made at surgery, as the localized stenosis of the left pulmonary vein was misinterpreted as partial cor triatriatum by cardiac catheterization, cineangiocardiography and extensive echocardiographic studies. Surgical correction of all the defects was successful, but pulmonary vascular resistance was still increased 2 years after surgery.
Key Words: Pulmonary vein stenosis congenital pulmonary vascular resistance