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European Heart Journal 2003 24(21):1965-1991; doi:10.1016/S0195-668X(03)00479-2
Copyright © 2003 by the European Society of Cardiology.
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ACC/ESC Expert consensus document

American College of Cardiology/European Society of Cardiology Clinical Expert Consensus Document on Hypertrophic Cardiomyopathy

A report of the American College of Cardiology Foundation Task Force on Clinical Expert Consensus Documents and the European Society of Cardiology Committee for Practice Guidelines

Writing Committee Members, Barry J. Maron, (Co-Chair)a,b, William J. McKenna, (Co-Chair)a,b,*, Gordon K. Danielsona, Lukas J. Kappenbergera,b,*, Horst J. Kuhnb,*, Christine E. Seidman, Pravin M. Shaha, William H. Spencer, IIIa, Paolo Spiritoa,b,*, Folkert J. Ten Catea,b,* and E. Douglas Wiglea

ACCF Task Force on Clinical Expert Consensus Documents Members, Robert A. Vogel, (Chair), Jonathan Abrams, Eric R. Bates, Bruce R. Brodie{dagger}, Peter G. Danias{dagger}, Gabriel Gregoratos, Mark A. Hlatky, Judith S. Hochman, Sanjiv Kaul, Robert C. Lichtenberg, Jonathan R. Lindner, Robert A. O’Rourke{ddagger}, Gerald M. Pohost, Richard S. Schofield, Cynthia M. Tracy{dagger} and William L. Winters, Jr{dagger}

ESC Committee for Practice Guidelines Members*, Werner W. Klein, (Chair), Silvia G. Priori, (Co-Chair), Angeles Alonso-Garcia, Carina Blomström-Lundqvist, Guy De Backer, Jaap Deckers, Markus Flather, Jaromir Hradec, Ali Oto, Alexander Parkhomenko, Sigmund Silber and Adam Torbicki

The first 150 words of the full text of this article appear below.

Table of contents

Preamble
Introduction
    Organization of committee and evidence review
    Purpose of this Expert Consensus Document
General considerations and perspectives
Nomenclature, definitions, and clinical diagnosis
Obstruction to LV Outflow
Genetics and molecular diagnosis
General considerations for natural history, and clinical course
Symptoms and pharmacological managementstrategies
    Beta-adrenergic blocking agents
    Verapamil
    Disopyramide
    Drugs in end-stage phase
    Asymptomatic patients
    Infective endocarditis prophylaxis
    Pregnancy
Treatment options for drug-refractory patients
Additional approaches to relieve outflowobstruction and symptoms
    Dual-chamber pacing
    Percutaneous alcohol septal ablation
Sudden Cardiac Death
    Risk stratification
    Prevention
    Athlete recommendations
Atrial Fibrillation
References

Preamble

This document has been developed as a Clinical Expert Consensus Document (CECD), combining the resources of the American College of Cardiology Foundation (ACCF) and the European Society of Cardiology (ESC). It is intended to provide a perspective on the current state of management of patients with hypertrophic cardiomyopathy. Clinical Expert Consensus Documents are intended to inform practitioners, payers, and other interested parties of . . . [Full Text of this Article]

Introduction

Organization of committee and evidence review
Purpose of this Expert Consensus Document
General considerations and perspectives

Nomenclature, definitions, and clinical diagnosis

Obstruction to LV Outflow

Genetics and molecular diagnosis

General considerations for natural history, and clinical course

Symptoms and pharmacological management strategies

Beta-adrenergic blocking agents
Verapamil
Disopyramide
Drugs in end-stage phase
Asymptomatic patients
Infective endocarditis prophylaxis
Pregnancy
Treatment options for drug-refractory patients

Additional approaches to relieve outflow obstruction and symptoms

Dual-chamber pacing
Percutaneous alcohol septal ablation
Sudden Cardiac Death

Risk stratification
Prevention
Athlete recommendations
Atrial Fibrillation


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