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European Heart Journal 2004 25(6):531-534; doi:10.1016/j.ehj.2003.12.025
Copyright © 2004 by the European Society of Cardiology.
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Special Article

Arrhythmogenic right ventricular cardiomyopathy: clinical registry and database, evaluation of therapies, pathology registry, DNA banking

Cristina Bassoa, Thomas Wichterb, Gian A Danielic, Domenico Corradod, Elzbieta Czarnowskae, Guy Fontainef, William J McKennag, Andrea Navad, Nikos Protonotariosh, Loizos Antoniadesi, Katharzyna Wlodarskaj, Fabio D'Alessia and Gaetano Thienea,*,1

a Institute of Pathological Anatomy, University of Padua, Italy
b Department of Cardiology and Angiology, University Hospital of Münster, Germany
c Department of Biology, University of Padua, Italy
d Department of Clinical and Experimental Medicine, University of Padua, Italy
e Department of Pathology, Children's Memorial Health Institute, Warsaw, Poland
f Institute de Cardiologie, Group Hospitalier Pitiè-Salpetriere, Paris, France
g The Heart Hospital, University College of London, UK
h Yannis Protonotarios Medical Center, Naxos, Greece
i Department of Cardiology, Nicosia General Hospital, Cyprus
j Department of Noninvasive Cardiology and Congenital Heart Defects, Poland

* Corresponding author. Tel.: +39-49-8272286; fax: +39-49-8272284
E-mail address: cardpath@unipd.it

The first 10% of the full text of this article appears below.

A multidisciplinary collaborative European study has been designed with the aim to investigate the clinical, pathological and genetic features of arrhythmogenic right ventricular cardiomyopathy (ARVC), which is a progressive, genetically determined disorder of the right ventricular myocardium and a major risk of sudden death particularly in the young.1–3 The disease is reported familial up to 50% with autosomal dominant inheritance while an autosomal recessive form (Naxos disease) associated with cutaneous abnormalities also exists. Nine genetic loci and mutations in three genes have been discovered so far.4–7 Treatment and prevention of ventricular tachyarrhythmias and sudden death include antiarrhythmic drug therapy, catheter ablation and the implantable cardioverter-defibrillator.2,8–11 However, a systematic evaluation of treatment options is not yet available.

. . . [Full Text of this Article]

Objectives

Financial support and project management

Ethical aspects

Preliminary achievements, exploitation and mid-term review

International collaborations

Call for other European cardiologist/scientists


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